Carnitine O-palmitoyltransferase

Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme (EC 2.3.1.21) involved in the metabolism of palmitoylcarnitine into palmitoyl-CoA. A related transferase is carnitine acyltransferase.

Molecules

Pathway

Human forms

There are four different forms of CPT in humans:

• CPT1A – associated with Carnitine palmitoyltransferase I deficiency
• CPT1B
• CPT1C
• CPT2 – associated with carnitine palmitoyltransferase II deficiency

See also

• Fatty acid degradation § Transport into the mitochondrial matrix

References

External links

• PDOC00402 – Acyltransferases ChoActase / COT / CPT family in PROSITE
• Choline/Carnitine o-acyltransferase family in Pfam
• UMich Orientation of Proteins in Membranes protein/pdbid-2h4t
• Carnitine+O-Palmitoyltransferase at the U.S. National Library of Medicine Medical Subject Headings (MeSH)